Otosclerosis Health Dictionary

Otosclerosis: From 3 Different Sources


A disorder of the middle ear that causes progressive deafness. The condition usually develops in both ears. Otosclerosis occurs when overgrowth of bone immobilizes the stapes (the innermost one of the three tiny bones in the middle ear). As a result, sound vibrations are prevented from passing along the bone to the inner ear. To an affected person, sounds are muffled but can be distinguished more easily if there is background noise.

Otosclerosis frequently runs in families, and symptoms usually start to appear in early adulthood. The condition affects more women than men, and often develops during pregnancy. Hearing loss progresses slowly over 10 to 15 years and is often accompanied by tinnitus and, more rarely, vertigo. A degree of sensorineural deafness may develop, making high tones difficult to hear and causing the sufferer to speak loudly.

The condition is diagnosed by hearing tests. It can be cured by stapedectomy, a surgical procedure in which the stapes is replaced by a tiny piston, which moves through a hole created in the inner ear. Because the piston can move freely, it can transmit sound vibrations to the inner ear. Alternatively, a hearingaid can markedly improve hearing.

Health Source: BMA Medical Dictionary
Author: The British Medical Association
(otospongiosis) n. a disorder causing conductive *deafness in adult life. An overgrowth of the bone of the inner ear leads to the third ear ossicle (the stapes) becoming fixed to the fenestra ovalis, which separates the middle and inner ears, so that sounds cannot be conducted to the inner ear. Deafness is progressive and may become very severe, but treatment by surgery is usually highly effective (see fenestration; stapedectomy). Nonsurgical treatments include fluoride tablets and the provision of suitable *hearing aids.
Health Source: Oxford | Concise Colour Medical Dictionary
Author: Jonathan Law, Elizabeth Martin

Stapedectomy

An operation on the middle EAR to remove the STAPES and replace it with an arti?cial alternative. The procedure is aimed at treating DEAFNESS caused by otosclerosis in which the stapes becomes ?xed by an overgrowth of bone, preventing it from transmitting sound. Stapedectomy improves hearing in around 90 per cent of those people who have the operation. (See EAR, DISEASES OF.)... stapedectomy

Fenestration

A largely obsolete surgical operation to form a new opening in the bony LABYRINTH of the inner ear in the treatment of deafness caused by otosclerosis (see under EAR, DISEASES OF). Nowadays the disorder is usually surgically treated by STAPEDECTOMY.... fenestration

Ear, Diseases Of

Diseases may affect the EAR alone or as part of a more generalised condition. The disease may affect the outer, middle or inner ear or a combination of these.

Examination of the ear includes inspection of the external ear. An auriscope is used to examine the external ear canal and the ear drum. If a more detailed inspection is required, a microscope may be used to improve illumination and magni?cation.

Tuning-fork or Rinne tests are performed to identify the presence of DEAFNESS. The examiner tests whether the vibrating fork is audible at the meatus, and then the foot of the fork is placed on the mastoid bone of the ear to discover at which of the two sites the patient can hear the vibrations for the longest time. This can help to di?erentiate between conductive and nerve deafness.

Hearing tests are carried out to determine the level of hearing. An audiometer is used to deliver a series of short tones of varying frequency to the ear, either through a pair of headphones or via a sound transducer applied directly to the skull. The intensity of the sound is gradually reduced until it is no longer heard and this represents the threshold of hearing, at that frequency, through air and bone respectively. It may be necessary to play a masking noise into the opposite ear to prevent that ear from hearing the tones, enabling each ear to be tested independently.

General symptoms The following are some of the chief symptoms of ear disease: DEAFNESS (see DEAFNESS). EARACHE is most commonly due to acute in?ammation of the middle ear. Perceived pain in this region may be referred from other areas, such as the earache commonly experienced after tonsillectomy (removal of the TONSILS) or that caused by carious teeth (see TEETH, DISORDERS OF). The treatment will depend on the underlying cause. TINNITUS or ringing in the ear often accompanies deafness, but is sometimes the only symptom of ear disease. Even normal people sometimes experience tinnitus, particularly if put in soundproofed surroundings. It may be described as hissing, buzzing, the sound of the sea, or of bells. The intensity of the tinnitis usually ?uctuates, sometimes disappearing altogether. It may occur in almost any form of ear disease, but is particularly troublesome in nerve deafness due to ageing and in noise-induced deafness. The symptom seems to originate in the brain’s subcortical regions, high in the central nervous system. It may be a symptom of general diseases such as ANAEMIA, high blood pressure and arterial disease, in which cases it is often synchronous with the pulse, and may also be caused by drugs such as QUININE, salicylates (SALICYLIC ACID and its salts, for example, ASPIRIN) and certain ANTIBIOTICS. Treatment of any underlying ear disorder or systemic disease, including DEPRESSION, may reduce or even cure the tinnitis, but unfortunately in many cases the noises persist. Management involves psychological techniques and initially an explanation of the mechanism and reassurance that tinnitus does not signify brain disease, or an impending STROKE, may help the person. Tinnitus maskers – which look like hearing aids – have long been used with a suitably pitched sound helping to ‘mask’ the condition.

Diseases of the external ear

WAX (cerumen) is produced by specialised glands in the outer part of the ear canal only. Impacted wax within the ear canal can cause deafness, tinnitis and sometimes disturbance of balance. Wax can sometimes be softened with olive oil, 5-per-cent bicarbonate of soda or commercially prepared drops, and it will gradually liquefy and ‘remove itself’. If this is ineffective, syringing by a doctor or nurse will usually remove the wax but sometimes it is necessary for a specialist (otologist) to remove it manually with instruments. Syringing should not be done if perforation of the tympanic membrane (eardrum) is suspected. FOREIGN BODIES such as peas, beads or buttons may be found in the external ear canal, especially in children who have usually introduced them themselves. Live insects may also be trapped in the external canal causing intense irritation and noise, and in such cases spirit drops are ?rst instilled into the ear to kill the insect. Except in foreign bodies of vegetable origin, where swelling and pain may occur, syringing may be used to remove some foreign bodies, but often removal by a specialist using suitable instrumentation and an operating microscope is required. In children, a general anaesthetic may be needed. ACUTE OTITIS EXTERNA may be a di?use in?ammation or a boil (furuncle) occurring in the outer ear canal. The pinna is usually tender on movement (unlike acute otitis media – see below) and a discharge may be present. Initially treatment should be local, using magnesium sulphate paste or glycerine and 10-per-cent ichthaminol. Topical antibiotic drops can be used and sometimes antibiotics by mouth are necessary, especially if infection is acute. Clotrimazole drops are a useful antifungal treatment. Analgesics and locally applied warmth should relieve the pain.

CHRONIC OTITIS EXTERNA producing pain and discharge, can be caused by eczema, seborrhoeic DERMATITIS or PSORIASIS. Hair lotions and cosmetic preparations may trigger local allergic reactions in the external ear, and the chronic disorder may be the result of swimming or use of dirty towels. Careful cleaning of the ear by an ENT (Ear, Nose & Throat) surgeon and topical antibiotic or antifungal agents – along with removal of any precipitating cause – are the usual treatments. TUMOURS of the ear can arise in the skin of the auricle, often as a result of exposure to sunlight, and can be benign or malignant. Within the ear canal itself, the commonest tumours are benign outgrowths from the surrounding bone, said to occur in swimmers as a result of repeated exposure to cold water. Polyps may result from chronic infection of the ear canal and drum, particularly in the presence of a perforation. These polyps are soft and may be large enough to ?ll the ear canal, but may shrink considerably after treatment of the associated infection.

Diseases of the middle ear

OTITIS MEDIA or infection of the middle ear, usually occurs as a result of infection spreading up the Eustachian tubes from the nose, throat or sinuses. It may follow a cold, tonsillitis or sinusitis, and may also be caused by swimming and diving where water and infected secretions are forced up the Eustachian tube into the middle ear. Primarily it is a disease of children, with as many as 1.5 million cases occurring in Britain every year. Pain may be intense and throbbing or sharp in character. The condition is accompanied by deafness, fever and often TINNITUS.

In infants, crying may be the only sign that something is wrong – though this is usually accompanied by some localising manifestation such as rubbing or pulling at the ear. Examination of the ear usually reveals redness, and sometimes bulging, of the ear drum. In the early stages there is no discharge, but in the later stages there may be a discharge from perforation of the ear drum as a result of the pressure created in the middle ear by the accumulated pus. This is usually accompanied by an immediate reduction in pain.

Treatment consists of the immediate administration of an antibiotic, usually one of the penicillins (e.g. amoxicillin). In the majority of cases no further treatment is required, but if this does not quickly bring relief then it may be necessary to perform a myringotomy, or incision of the ear drum, to drain pus from the middle ear. When otitis media is treated immediately with su?cient dosage of the appropriate antibiotic, the chances of any permanent damage to the ear or to hearing are reduced to a negligible degree, as is the risk of any complications such as mastoiditis (discussed later in this section). CHRONIC OTITIS MEDIA WITH EFFUSION or glue ear, is the most common in?ammatory condition of the middle ear in children, to the extent that one in four children in the UK entering school has had an episode of ‘glue ear’. It is characterised by a persistent sticky ?uid in the middle ear (hence the name); this causes a conductive-type deafness. It may be associated with enlarged adenoids (see NOSE, DISORDERS OF) which impair the function of the Eustachian tube. If the hearing impairment is persistent and causes problems, drainage of the ?uid, along with antibiotic treatment, may be needed – possibly in conjunction with removal of the adenoids. The insertion of grommets (ventilation tubes) was for a time standard treatment, but while hearing is often restored, there may be no long-term gain and even a risk of damage to the tympanic membrane, so the operation is less popular than it was a decade or so ago. MASTOIDITIS is a serious complication of in?ammation of the middle ear, the incidence of which has been dramatically reduced by the introduction of antibiotics. In?ammation in this cavity usually arises by direct spread of acute or chronic in?ammation from the middle ear. The signs of this condition include swelling and tenderness of the skin behind the ear, redness and swelling inside the ear, pain in the side of the head, high fever, and a discharge from the ear. The management of this condition in the ?rst instance is with antibiotics, usually given intravenously; however, if the condition fails to improve, surgical treatment is necessary. This involves draining any pus from the middle ear and mastoid, and removing diseased lining and bone from the mastoid.

Diseases of the inner ear

MENIÈRE’S DISEASE is a common idiopathic disorder of ENDOLYMPH control in the semicircular canals (see EAR), characterised by the triad of episodic VERTIGO with deafness and tinnitus. The cause is unknown and usually one ear only is affected at ?rst, but eventually the opposite ear is affected in approximately 50 per cent of cases. The onset of dizziness is often sudden and lasts for up to 24 hours. The hearing loss is temporary in the early stages, but with each attack there may be a progressive nerve deafness. Nausea and vomiting often occur. Treatment during the attacks includes rest and drugs to control sickness. Vasodilator drugs such as betahistine hydrochloride may be helpful. Surgical treatment is sometimes required if crippling attacks of dizziness persist despite these measures. OTOSCLEROSIS A disorder of the middle ear that results in progressive deafness. Often running in families, otosclerosis affects about one person in 200; it customarily occurs early in adult life. An overgrowth of bone ?xes the stapes (the innermost bone of the middle ear) and stops sound vibrations from being transmitted to the inner ear. The result is conductive deafness. The disorder usually affects both ears. Those affected tend to talk quietly and deafness increases over a 10–15 year period. Tinnitus often occurs, and occasionally vertigo.

Abnormal hearing tests point to the diagnosis; the deafness may be partially overcome with a hearing aid but surgery is eventually needed. This involves replacing the stapes bone with a synthetic substitute (stapedectomy). (See also OTIC BAROTRAUMA.)... ear, diseases of

Hearing Loss

Otosclerosis: a common cause of deafness in healthy adults. Gradual progressive hearing loss with troublesome tinnitus. The stapes may be fixed and the cochlea damaged. Bones may become spongy and demineralised. While deafness is a matter for the professional specialist, herbal treatment may prove useful. Examine ear for wax.

Internal. Elderflower and Peppermint tea (catarrhal). Ginkgo tea.

Tablets/capsules. Ginkgo. Improvement reported in moderate loss.

Topical. Garlic oil. Injection of 3-4 drops at night.

Wax in the ear. Mixture: 30 drops oil Eucalyptus, 1 drop Tincture Capsicum (or 3 of Ginger), 1oz (30ml) Olive oil. Inject 4-5 drops, warm.

Black Cohosh Drops. It is claimed that John Christopher (USA) improved many cases of moderate hearing loss with topical use of 5-10 drops Liquid Extract in 1oz oil of Mullein (or Olive oil).

Pulsatilla Drops. Tincture Pulsatilla and glycerol 50/50. 2-3 drops injected at bedtime. Assists auditory nerve function. (Arthur Hyde)

Nerve deafness due to fibroma of the 8th cranial nerve, or after surgery – oral: Mistletoe tea for temporary relief. ... hearing loss

Deafness

Complete or partial loss of hearing in 1 or both ears. There are 2 types of deafness: conductive deafness, which results from faulty propagation of sound from the outer to the inner ear; and sensorineural deafness, in which there is a failure in transmission of sounds to the brain. Hearing tests can determine whether deafness is conductive or sensorineural.

The most common cause of conductive deafness in adults is earwax. Otosclerosis is a less common cause and is usually treated by an operation called stapedectomy, in which the stapes (a small bone in the middle ear) is replaced with an artificial substitute. In a child, conductive deafness usually results from otitis media or glue ear. This condition may be treated by surgery (see myringotomy). In rare cases, deafness results from a perforated eardrum (see eardrum, perforated). Sensorineural deafness may be present from birth. This type of deafness may result from a birth injury or damage resulting from maternal infection with rubella at an early stage of pregnancy. Inner-ear damage may also occur soon after birth as the result of severe jaundice. Deafness at birth is incurable. Many children who are born deaf can learn to communicate effectively, often by using sign language. Cochlear implants may help those children born profoundly deaf to learn speech.

In later life, sensorineural deafness can be due to damage to the cochlea and/or labyrinth. It may result from prolonged exposure to loud noise, to Ménière’s disease, to certain drugs, or to some viral infections. The cochlea and labyrinth also degenerate naturally with old age, resulting in presbyacusis. Sensorineural deafness due to damage to the acoustic nerve may be the result of an acoustic neuroma. Deafness may be accompanied by tinnitus and vertigo. Sometimes it can lead to depression.

People with sensorineural deafness usually need hearing-aids to increase the volume of sound reaching the inner ear. Lip-reading is invaluable for deaf people. Other aids, such as an amplifier for the earpiece of a telephone, are available. (See also ear; hearing.)... deafness

Ear, Disorders Of

The ear is susceptible to various disorders, some of which can lead to deafness. In rare cases, the ear canal, ossicles in the middle ear, or pinna are absent or deformed at birth. Rubella in early pregnancy can damage the baby’s developing ear, leading to deafness. Most cases of congenital sensorineural deafness are genetic.

Infection is the most common cause of ear disorders; it may occur in the ear canal, leading to otitis externa, or affect the middle ear, causing otitis media. This can lead to perforation of the eardrum (see eardrum, perforated). Persistent glue ear, often due to infection, is the most common cause of childhood hearing difficulties. Viral infection of the inner ear may cause labyrinthitis.

Cauliflower ear is the result of one large or several small injuries to the pinna. Perforation of the eardrum can result from poking objects into the ear or loud noise. Prolonged exposure to loud noise can cause tinnitus and/or deafness. Pressure changes associated with flying or scuba diving can also cause minor damage (see barotrauma).Tumours of the ear are rare. Acoustic neuroma is a noncancerous tumour of the acoustic nerve that may press on structures in the ear to cause deafness, tinnitus, and problems with balance.

In cholesteatoma, skin cells and debris collect in the middle ear. Obstruction of the ear canal is most often the result of earwax, although in small children, an object may have been pushed into the ear (see ear, foreign body in).

In otosclerosis, a hereditary condition, a bone in the middle ear becomes fixed, causing deafness. Meniérè’s disease is an uncommon condition in which deafness, vertigo, and tinnitus result from the accumulation of fluid in the inner ear. Deafness in many elderly people is due to presbyacusis, in which hair cells in the cochlea deteriorate.

Certain drugs, such as aminoglycoside drugs and some diuretic drugs, can damage ear function.... ear, disorders of

Otorhinolaryngology

A surgical speciality, also known as surgery, that is concerned with diseases of the ear, nose, and throat. specialists treat

sinus problems, otitis media, glue ear, tonsillitis, minor hearing loss, otosclerosis, Ménière’s disease, airway problems in children, uncontrollable nosebleeds, and cancer of the larynx and sinuses.... otorhinolaryngology

Stapes

The innermost of the 3 tiny, sound-conducting bones in the middle ear. The stapes is the smallest bone in the body. Its head articulates with the incus, and its base fits into the oval window in the wall of the inner ear.

In otosclerosis, the stapes becomes fixed and cannot transmit sound to the inner ear. Resultant hearing loss can be treated by stapedectomy.... stapes

Oral Contraceptives

A group of oral drug preparations containing one or more synthetic female sex hormones, taken by women in a monthly cycle to prevent pregnancy. “The pill” commonly refers to the combined or the phased pill, which both contain an oestrogen drug and a progestogen drug, and the minipill, which contains only a progestogen. Oestrogen pills include ethinylestradiol; progestogens include levonorgestrel and norethisterone. When used correctly, the number of pregnancies among women using oral contraceptives for one year is less than 1 per cent. Actual failure rates may be 4 times higher, particularly for the minipill, which has to be taken at precisely the same time each day.

Combined and phased pills increase oestrogen and progesterone levels. This interferes with the production of two hormones, luteinizing hormone (LH) and follicle-stimulating hormone (FSH), which in turn prevents ovulation. The minipill works mainly by making the mucus lining of the cervix too thick to be penetrated by sperm.

Oestrogen-containing pills offer protection against uterine and ovarian cancer, ovarian cysts, endometriosis, and irondeficiency anaemia. They also tend to make menstrual periods regular, lighter, and relatively pain-free. Possible side effects include nausea, weight gain, depression, swollen breasts, reduced sex drive, increased appetite, leg and abdominal cramps, headaches, and dizziness. More seriously, there is a risk of thrombosis causing a stroke or a pulmonary embolism. These pills may also aggravate heart disease or cause hypertension, gallstones, jaundice, and, very rarely, liver cancer. All oral contraceptives can cause bleeding between periods, especially the minipill. Other possible adverse effects of the minipill include irregular periods, ectopic pregnancy, and ovarian cysts. There may be a slightly increased long-term risk of breast cancer for women taking the combined pill.

Oestrogen-based pills should generally be avoided in women with hypertension, hyperlipidaemia, liver disease, migraine, otosclerosis, or who are at increased risk of a thrombosis. They are not usually prescribed to a woman with a personal or family history of heart or circulatory disorders, or who suffers from unexplained vaginal bleeding. The minipill or a lowoestrogen pill may be used by women who should avoid oestrogens. Combined or phased pills may interfere with milk production and should not be taken during breast-feeding. Certain drugs may impair the effectiveness of oral contraceptives. (See also contraception.) ... oral contraceptives

Osteogenesis Imperfecta

A congenital condition characterized by abnormally brittle bones that are unusually susceptible to fractures. The condition is caused by an inherited defect in the connective tissue that forms the basic material of bone. Severely affected infants are born with multiple fractures and a soft skull and do not usually survive. Others have many fractures during infancy and childhood, often as a result of normal handling and activities, and it may be difficult to distinguish the condition from child abuse. A common sign of the condition is that the whites of the eyes are abnormally thin, making them appear blue. Sufferers may also be deaf due to otosclerosis. Very mild cases may not be detected until adolescence or later.

There is no specific treatment. Fractures are immobilized and usually heal quickly, but they may cause shortening and deformity of the limbs, resulting in abnormal, stunted growth. Skull fractures may cause brain damage or death. Parents may have genetic counselling to estimate the risk in future children. Severe cases can be diagnosed prenatally by ultrasound scanning.... osteogenesis imperfecta

Tinnitus

A ringing, buzzing, whistling, hissing, or other noise heard in the ear or ears in the absence of a noise in the environment. Tinnitus is almost always associated with hearing loss, particularly that due to presbyacusis and exposure to loud noise. It can also occur as a symptom of ear disorders such as labyrinthitis, Ménière’s disease, otitis media, otosclerosis, ototoxicity, and blockage of the ear canal with earwax. It may also be caused by certain drugs, such as aspirin or quinine, or may follow a head injury.Any underlying disorder is treated if possible.

Many sufferers make use of a radio, television, cassette player, or headphones to block out the noise in their ears.

A tinnitus masker, a hearingaid type device that plays white noise (a random mixture of sounds at a wide range of frequencies), may be effective.... tinnitus

Hearing Therapy

the support and rehabilitation of people with hearing difficulties, tinnitus, or vertigo. It includes supplying help with acclimatizing to *hearing aids, teaching lip-reading, advising on *environmental hearing aids, and offering general information and advice regarding the auditory system. Other functions are to explain such conditions as *Ménière’s disease and *otosclerosis and to provide *tinnitus retraining therapy (TRT) and other forms of tinnitus management.... hearing therapy

Otospongiosis

n. see otosclerosis.... otospongiosis



Recent Searches